Bolger Alexandra Amy, Stewart Paul Anthony
From the Department of Anaesthetics, Alfred Hospital, Melbourne, Victoria, Australia.
The University of Sydney, Sydney, New South Wales, Australia.
A A Pract. 2019 Aug 15;13(4):126-129. doi: 10.1213/XAA.0000000000001010.
Hereditary neuropathy with liability to pressure palsies is an autosomal dominant condition occurring in up to 16 per 100,000 people and predisposes to neural compressive injury. Given the rarity of this condition, no guidelines currently exist for the anesthetic management of hereditary neuropathy with liability to pressure palsies. We describe the management of analgesia during labor in a woman diagnosed with hereditary neuropathy with liability to pressure palsies and a history of nerve palsy after obstetric anesthesia. Our report highlights the necessity of clinician awareness of hereditary neuropathy with liability to pressure palsies and the anesthetic precautions used to successfully avoid neural injury in this case.
遗传性压力易感性周围神经病是一种常染色体显性疾病,发病率高达十万分之十六,易导致神经受压损伤。鉴于该疾病罕见,目前尚无关于遗传性压力易感性周围神经病麻醉管理的指南。我们描述了一名被诊断为遗传性压力易感性周围神经病且有产科麻醉后神经麻痹病史的女性在分娩期间的镇痛管理。我们的报告强调了临床医生了解遗传性压力易感性周围神经病的必要性以及在该病例中为成功避免神经损伤所采取的麻醉预防措施。