Pabich Samantha, Flynn Maxfield, Pelley Elaine
Division of Endocrinology, Diabetes and Metabolism, University of Wisconsin School of Medicine and Public Health, Madison, Wisconsin.
J Endocr Soc. 2019 Mar 18;3(5):882-886. doi: 10.1210/js.2018-00406. eCollection 2019 May 1.
Management of diabetes insipidus (DI) is usually facilitated by an intact thirst mechanism prompting water ingestion in times of rising osmolality. Maintenance of eunatremia can be quite difficult in patients with DI and adipsia because of the absence of this homeostatic mechanism. Few published protocols for management of these complex cases exist. We report a case of a 16-year-old girl who had a diagnosis of craniopharyngioma with preoperative hypopituitarism and central DI. She underwent transsphenoidal resection in 2013 and additionally developed postoperative cognitive impairment and hypothalamic dysfunction, including adipsia. She subsequently experienced widely dysregulated sodium levels, necessitating inpatient care ∼30% of days in 2014 and 2015. We created a protocol for this patient that uses a fixed daily dose of subcutaneous DDAVP combined with daily modulation of fluid intake based on daily serum sodium measurement. The protocol provides guidance for the day's fluid intake based on both the current sodium result and the rate of change from the previous day. Since the adoption of the protocol in June 2016, the patient has had a dramatic reduction in hospitalizations. Use of a protocol for providing recommendations for fluid intake based on the sodium level and rate of change may help to maintain normal sodium levels in such patients, decreasing hospitalization and improving quality of life.
尿崩症(DI)的管理通常因完整的口渴机制而变得容易,该机制会在渗透压升高时促使机体摄入水分。对于患有尿崩症且无渴感的患者,由于缺乏这种稳态机制,维持正常血钠水平可能相当困难。目前几乎没有已发表的针对这些复杂病例的管理方案。我们报告了一例16岁女孩的病例,她被诊断为颅咽管瘤,术前存在垂体功能减退和中枢性尿崩症。她于2013年接受了经蝶窦切除术,术后还出现了认知障碍和下丘脑功能障碍,包括无渴感。随后,她的血钠水平出现了广泛的失调,在2014年和2015年,约30%的时间需要住院治疗。我们为该患者制定了一个方案,即使用固定的每日皮下注射去氨加压素剂量,并根据每日血清钠测量结果对液体摄入量进行每日调整。该方案根据当前的钠结果以及与前一天的变化率为当天的液体摄入量提供指导。自2016年6月采用该方案以来,患者的住院次数大幅减少。使用基于钠水平和变化率来提供液体摄入建议的方案可能有助于维持此类患者的正常钠水平,减少住院次数并改善生活质量。