Bajracharya Leena, Lama Ang Jangmu
Tilganga Institute of Ophthalmology.
Nepal J Ophthalmol. 2018 Jan;10(19):82-85. doi: 10.3126/nepjoph.v10i1.21718.
Keratoconus has been known to be associated with various ocular conditions.
To describe a case of high hyperopia, keratoconus and pigmentary retinopathy.
An eight year old boy, whose initial refractive error was high hyperopia with short axial length of 20mm, presented as bilateral advanced keratoconus with acute hydrops in one eye. Subsequently his other eye also developed hydrops. He had nystagmus and pigmentary retinopathy from his infancy. He was managed conservatively and the hydrops resolved in both the eyes leaving paracentral scar in the cornea.
The triad of keratoconus, high hyperopia and pigmentary retinopathy has been quite rare. There could be syndromic association between the three simultaneous ocular findings.
圆锥角膜已知与多种眼部疾病相关。
描述一例高度远视、圆锥角膜和色素性视网膜病变的病例。
一名8岁男孩，初始屈光不正为高度远视，眼轴短，仅20mm，表现为双眼晚期圆锥角膜，其中一只眼睛出现急性角膜水肿。随后，他的另一只眼睛也出现了水肿。他自幼患有眼球震颤和色素性视网膜病变。对他进行了保守治疗，双眼的角膜水肿均已消退，但角膜留下了旁中心瘢痕。
圆锥角膜、高度远视和色素性视网膜病变三联征相当罕见。这三种同时出现的眼部表现之间可能存在综合征关联。
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