Pediatric Neurosurgery, Hospital Universitário Onofre Lopes, Natal, Brazil; Department of Integrated Medicine, Federal University of Rio Grande do Norte, Natal, Brazil; Santos Dumont Institute, Macaíba, Brazil.
Department of Integrated Medicine, Federal University of Rio Grande do Norte, Natal, Brazil.
World Neurosurg. 2019 Aug;128:454-457. doi: 10.1016/j.wneu.2019.05.138. Epub 2019 May 24.
Endoscopic third ventriculostomy (ETV) is an option for hydrocephalus treatment in patients with myelomeningocele, mostly after a previous shunt dysfunction. Late failure of ETV is a rare event, traditionally associated with dramatic symptoms of intracranial hypertension. In patients with myelodysplasia and neurogenic bladder dysfunction, urodynamic deterioration can be a signal of neurologic worsening as a consequence of tethered cord or shunt problems.
We describe here a rare case of a 12-year-old female patient with myelomeningocele and evidence of a failure 10 years after a previously successful ETV whose initial symptoms were worsening of urinary complaints. After 2 months, she was admitted to the emergency department with seizures and acute hydrocephalus and was shunted.
Pediatric neurosurgeons must follow myelomeningocele patients with successful ETV for a long time and take care of subtle alterations of organic functions that have a close relationship with central nervous system integrity. A multidisciplinary approach can facilitate this strategy and avoid a tragic outcome.
内镜第三脑室造瘘术(ETV)是治疗脊髓脊膜膨出患者脑积水的一种选择,主要是在先前分流功能障碍之后。ETV 的晚期失败是一种罕见事件,传统上与颅内压升高的明显症状相关。在脊髓发育不良和神经性膀胱功能障碍的患者中,尿动力学恶化可能是由于拴系脊髓或分流问题导致神经恶化的信号。
我们在此描述了一例罕见的 12 岁女性患者,患有脊髓脊膜膨出,在先前成功的 ETV 后 10 年出现失败迹象,最初的症状是尿路问题恶化。2 个月后,她因癫痫发作和急性脑积水而被紧急送往急诊室,并进行了分流。
小儿神经外科医生必须对成功进行 ETV 的脊髓脊膜膨出患者进行长期随访,并注意与中枢神经系统完整性密切相关的细微的器官功能改变。多学科方法可以促进这一策略并避免悲惨的结局。