Kylat Ranjit I, Samson Ricardo A
Department of Pediatrics The University of Arizona College of Medicine Tucson Arizona.
Chidren's Heart Center of Nevada Las Vegas Nevada.
J Arrhythm. 2019 May 15;35(3):494-498. doi: 10.1002/joa3.12193. eCollection 2019 Jun.
Permanent junctional reciprocating tachycardia (PJRT) is a rare form of supraventricular tachycardia (SVT). It generally presents in infants but can be difficult to diagnose. The characteristic EKG findings, response to Adenosine and persistence or frequent recurrences are helpful in making the diagnosis. It is usually difficult to manage with the initial and single medications used in SVT. Many patients are misdiagnosed and not treated effectively and end up having end stage cardiomyopathy and are diagnosed in patients referred for transplant. Hence all patients referred for a cardiac transplant with dilated cardiomyopathy need to be evaluated for this arrhythmia. If appropriate treatment is started early in the course, the failure can be ameliorated, and the cardiomyopathy can be resolved.
永久性交界性反复性心动过速（PJRT）是室上性心动过速（SVT）的一种罕见形式。它通常在婴儿期出现，但可能难以诊断。特征性的心电图表现、对腺苷的反应以及持续性或频繁复发有助于做出诊断。使用治疗室上性心动过速的初始单一药物通常难以对其进行管理。许多患者被误诊且未得到有效治疗，最终发展为终末期心肌病，在转诊进行移植的患者中被诊断出来。因此，所有因扩张型心肌病转诊进行心脏移植的患者都需要评估是否存在这种心律失常。如果在病程早期开始适当治疗，心力衰竭可以得到改善，心肌病也可以得到缓解。
