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经导管治疗儿童复杂先天性心脏病后天性冠状窦口闭锁

Transcatheter treatment of acquired coronary sinus ostium atresia in a child with complex congenital heart disease.

机构信息

Department of Pediatrics, Banner University Medical Center-Tucson/University of Arizona, Tucson, Arizona.

Department of Pediatrics (Cardiology), Banner University Medical Center-Tucson/University of Arizona, Tucson, Arizona.

出版信息

Catheter Cardiovasc Interv. 2020 Feb;95(2):E62-E65. doi: 10.1002/ccd.28489. Epub 2019 Sep 5.

Abstract

Congenital coronary sinus ostium atresia is a rare condition that is typically considered benign, as long as there is adequate drainage via another route. However, in children with single ventricle congenital heart disease, adequate drainage may not be assured after complex surgical interventions, putting them at risk for myocardial injury. We present a patient with complex single ventricle congenital heart disease who developed acquired coronary sinus ostium atresia after surgical intervention that was treated by a transcatheter approach to prevent the sequelae of coronary sinus hypertension.

摘要

先天性冠状窦口闭锁是一种罕见的情况,通常被认为是良性的,只要有足够的引流通过另一种途径。然而,在患有单心室先天性心脏病的儿童中,复杂的手术干预后可能无法保证充分的引流,使他们面临心肌损伤的风险。我们介绍了一位患有复杂单心室先天性心脏病的患者,他在手术后发生了获得性冠状窦口闭锁,通过经导管途径进行治疗,以预防冠状窦高压的后遗症。

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