眶睑部神经纤维瘤病的外科治疗

The surgical management of orbitopalpebral neurofibromatosis.

作者信息

Morax S, Herdan M L, Hurbli T

机构信息

Department of Ophthalmology and Oculo-plastic Surgery, Fondation Ophtalmologique Rothschild, Paris, France.

出版信息

Ophthalmic Plast Reconstr Surg. 1988;4(4):203-13. doi: 10.1097/00002341-198804040-00002.

DOI:10.1097/00002341-198804040-00002

PMID:3155319

Abstract

Orbitopalpebral neurofibromatosis may cause severe soft tissue deformity. Exophthalmos is either due to an intraorbital mass or to the absence of the greater wing of the sphenoid (mesodermal dysplasia). Five patients are presented. Surgical procedures and craniofacial techniques are detailed and discussed.

摘要

眶睑部神经纤维瘤病可导致严重的软组织畸形。眼球突出要么是由于眶内肿物，要么是由于蝶骨大翼缺失（中胚层发育异常）。本文介绍了5例患者。详细阐述并讨论了手术步骤及颅面技术。