Miyazaki Yumiko, Orisaka Makoto, Nishino Chihiro, Onuma Toshimichi, Kurokawa Tetsuji, Yoshida Yoshio
Department of Obstetrics and Gynecology, University of Fukui Faculty of Medical Sciences, Fukui, Japan.
J Obstet Gynaecol Res. 2020 Feb;46(2):347-351. doi: 10.1111/jog.14175. Epub 2019 Dec 9.
Herlyn-Werner-Wunderlich syndrome (HWWs) is a rare congenital malformation that involves uterus dideslphys, obstructed hemivagina and ipsilateral renal agenesis. The obstructed vagina affects menstrual flow and causes related clinical features after menarche. Pelvic endometriosis is one of the common complications of HWWs. Resection of the vaginal septum can release the obstruction and result in good outcomes. However, in the case of cervical atresia, a rare variant of HWWs, ipsilateral hysterectomy is recommended because it is difficult to canalize cervical atresia surgically. Here we present a case of HWWs with cervical atresia complicated with pelvic endometriosis. She was treated with laparoscopic ovarian cystectomy followed by hormonal therapy. Six months after surgery, there is no evidence of recurrence of endometrioma.
赫林-韦纳-温德利希综合征(HWWs)是一种罕见的先天性畸形,包括双子宫、阴道半段梗阻和同侧肾缺如。梗阻性阴道会影响月经血流,并在初潮后引起相关临床特征。盆腔子宫内膜异位症是HWWs的常见并发症之一。切除阴道纵隔可解除梗阻并取得良好效果。然而,对于HWWs的一种罕见变异型——宫颈闭锁,由于手术打通宫颈闭锁困难,建议行同侧子宫切除术。在此,我们报告一例伴有宫颈闭锁并合并盆腔子宫内膜异位症的HWWs病例。她接受了腹腔镜卵巢囊肿切除术,随后进行了激素治疗。术后6个月,没有子宫内膜瘤复发的迹象。