Riahi Hend, Barsaoui Maher, Zitouna Khaled
Tunis Med. 2019 Jul;97(7):870-873.
Osteochondroma is a developmental lesion rather than a true neoplasm. Osteochondromas are composed of cortical and medullary bone with an overlying hyaline cartilage cap and must demonstrate continuity with the underlying parent bone cortex and medullary canal. Osteochondromas may be solitary or multiple. We report the case of a patient carrying the here ditary form and who has presented a thoracic deformity and a progressive dyspnea for 5 months. Imaging was related to a bulky osteochondroma of the scapula responsible for thoracic deformity. Benign character was confirmed on the histology data and the resection was performed posteriorly with muscular preservation.
骨软骨瘤是一种发育性病变而非真正的肿瘤。骨软骨瘤由皮质骨和髓质骨组成,表面覆盖有透明软骨帽,且必须与下方的母骨皮质和髓腔相连。骨软骨瘤可单发或多发。我们报告了一例患有遗传性骨软骨瘤的患者,该患者出现胸廓畸形并进行性呼吸困难5个月。影像学检查显示为肩胛骨的巨大骨软骨瘤导致胸廓畸形。组织学检查证实为良性,遂行后路切除并保留肌肉。