Can Dang D T, Lepard Jacob R, Tri Tran T, Van Duong Tran, Thuy Nguyen T, Thach Pham N, Johnston James M, Oakes W Jerry, Dong A Tran
1Neurosurgical Department, Children's Hospital 2, and.
9University of Medicine and Pharmacy at Ho Chi Minh City, Vietnam.
J Neurosurg Pediatr. 2020 Jan 17;25(4):445-451. doi: 10.3171/2019.11.PEDS19291. Print 2020 Apr 1.
Conjoined twins are a rare congenital abnormality with an estimated incidence of 1:50,000 pregnancies and 1:200,000 live births. Pygopagus twins are characterized by sacrococcygeal fusion that is commonly associated with perineal and spinal abnormalities. Management of this complex disease requires a well-developed surgical system with multidisciplinary capacity and expertise.A decade ago there were no dedicated pediatric neurosurgeons in southern Vietnam. This has changed within a few short years; there are now 10 dedicated pediatric neurosurgeons with continually expanding technical capacity. In August 2017 a multidisciplinary surgical and anesthetic team successfully separated female pygopagus twins with fused sacrum and spinal cord with associated myelomeningocele defect.The authors present here the first successful separation of pygopagus twins in Vietnam as a representative case of gradual and sustainable pediatric neurosurgical scale-up.
联体双胎是一种罕见的先天性畸形,估计发生率为每50,000次妊娠中有1例,每200,000例活产中有1例。骶尾部联体双胎的特征是骶尾融合,通常伴有会阴和脊柱异常。这种复杂疾病的治疗需要一个具备多学科能力和专业知识的完善手术系统。十年前,越南南部没有专门的儿科神经外科医生。在短短几年内这种情况发生了变化;现在有10名专门的儿科神经外科医生,其技术能力在不断扩大。2017年8月,一个多学科手术和麻醉团队成功分离了一对骶骨和脊髓融合并伴有脊髓脊膜膨出缺损的女性骶尾部联体双胎。作者在此介绍越南首例成功分离骶尾部联体双胎的病例,作为儿科神经外科逐步且可持续扩大规模的一个典型案例。