Billet F, Bluemm R G, Beyer H K
Klinik für Radiologie des katholischen Marienhospitals Herne Ruhr-Universität Bochum.
Rontgenblatter. 1988 Aug;41(8):320-3.
MR is a sensitive noninvasive examination method for diagnosing parenchymatous cryptic arteriovenous malformations and sequels of cerebral haemorrhage. In a patient with recurring nosebleed and brain stem syndrome eleven so-called cryptic arteriovenous malformations or their haemorrhage sequels were diagnosed via magnetic resonance tomography. Basing on these specific findings, nosebleeding, and a positive family anamnesis, the findings could be classified as belonging to manifestations of Osler's disease (hereditary haemorrhagic telangiectasia). This rare disease is characterised by a triad of signs: telangiectasias, recurring bleeding, and heredity. In this article the specific MR image is compared with the CT pattern and the results are discussed against the background of literature on Osler's disease which is also known as Rendu-Osler-Weber disease.
磁共振成像(MR)是诊断实质性隐匿性动静脉畸形及脑出血后遗症的一种敏感的无创检查方法。在一名患有复发性鼻出血和脑干综合征的患者中,通过磁共振断层扫描诊断出11处所谓的隐匿性动静脉畸形或其出血后遗症。基于这些特定的发现、鼻出血以及阳性家族史,这些发现可归类为奥斯勒病(遗传性出血性毛细血管扩张症)的表现。这种罕见疾病的特征是三联征:毛细血管扩张、复发性出血和遗传。在本文中,将特定的MR图像与CT图像进行了比较,并结合关于奥斯勒病(也称为朗杜-奥斯勒-韦伯病)的文献背景对结果进行了讨论。