Division of Pediatric Cardiac Surgery, University Hospital Muenster, Muenster, Germany.
Gerhard-Domagk-Institute of Pathology, University Hospital Muenster, Muenster, Germany.
Pediatr Pulmonol. 2020 Jun;55(6):E1-E3. doi: 10.1002/ppul.24753. Epub 2020 Apr 3.
Cardiac myxomas are rare occurrences in pediatric populations, as are pulmonary artery aneurysms. We report a 17-year-old adolescent with right atrial cardiac myxoma and concomitant multiple peripheral pulmonary artery aneurysms. Histological examination indicated infiltration of the pulmonary artery wall through the embolic cardiac myxoma cells, thereby weakening it. This report highlights the probable causal relationship between these two entities, proposes the possible pathomechanism and presents the diagnostic and therapeutic dilemmas in the management of this condition.
心脏黏液瘤在儿科人群中较为罕见,肺动脉瘤也是如此。我们报告了一例 17 岁青少年患有右心房心脏黏液瘤和多个周围性肺动脉瘤。组织学检查表明,通过栓塞的心脏黏液瘤细胞浸润肺动脉壁,从而使其变弱。本报告强调了这两种实体之间可能存在因果关系,提出了可能的发病机制,并介绍了这种疾病治疗管理中的诊断和治疗难题。