Faculty of Medicine and Biomedical Sciences, University of Algarve.
Physical Medicine and Rehabilitation Department, Hospital and University Center of Algarve - CHUA, Faro, Portugal.
J Stroke Cerebrovasc Dis. 2020 Jul;29(7):104827. doi: 10.1016/j.jstrokecerebrovasdis.2020.104827. Epub 2020 May 6.
Cortical deafness is an extremely rare clinical manifestation that originates mainly from bilateral cortical lesions in the primary auditory cortex. Its main clinical manifestation is the bilateral sudden loss of hearing. Diagnosis is difficulty due to its rarity and similarity with other language and communication disorders, such as Wernicke's aphasia, auditory agnosia or verbal deafness. Herein, we present a case report of a young woman with a sudden bilateral loss of auditory comprehension. Initially, a psychiatric nature of the disorder was considered, but the persistence of the symptoms, lead to the diagnosis of cortical deafness secondary to bilateral ischemic lesions in both temporal lobes. Progressive improvement occurred and three months after the initial manifestations she manifested pure verbal deafness. Cortical deafness usually has a poor functional prognosis, with limited therapeutic options. Rehabilitation and speech therapy is recommended to improve the chance of patients achieving communication skills.
皮质性耳聋是一种极其罕见的临床表现,主要源于初级听觉皮质的双侧皮质病变。其主要临床表现为双侧突发性听力丧失。由于其罕见性及其与其他语言和交流障碍(如韦尼克失语症、听觉失认症或听觉性聋)的相似性,诊断较为困难。在此,我们报告了一例年轻女性双侧听觉理解突然丧失的病例。最初,考虑为精神障碍,但由于症状持续存在,最终诊断为双侧颞叶双侧缺血性病变继发的皮质性耳聋。病情逐渐好转,在最初症状出现三个月后,患者表现为单纯的听觉性聋。皮质性耳聋的功能预后通常较差,治疗选择有限。建议康复和语言治疗以提高患者获得沟通能力的机会。