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莫尔加尼疝

Morgagni Hernia

作者信息

Svetanoff Wendy Jo, Sharma Sanjeev, Rentea Rebecca M.

机构信息

Children's Mercy

Abstract

Morgagni hernia was first identified in 1761 by Giovanni Battista Morgagni, the founder of pathological anatomy. Anatomically, the diaphragm is a thin, dome-shaped, musculotendinous structure that separates the thoracic and abdominal cavities. Morgagni hernia is the rarest form of congenital diaphragmatic hernia (CDH), accounting for only 2% to 5% of cases. Diaphragmatic hernias include the Bochdalek, hiatal, and paraesophageal hernias. A Bochdalek hernia occurs due to a defect in the diaphragm's posterolateral region. A hiatal hernia has a defect at the esophageal hiatus; a paraesophageal hernia has a defect adjacent to the esophageal hiatus. A Morgagni hernia arises from an anterior, retrosternal diaphragmatic defect. The condition is rarer than the other CDH types. Morgagni hernias tend to be less symptomatic as pulmonary hypoplasia is uncommon, leading to a delayed diagnosis of these defects.

摘要

莫尔加尼疝于1761年由病理解剖学创始人乔瓦尼·巴蒂斯塔·莫尔加尼首次发现。从解剖学角度来看,膈肌是一个薄的、穹顶状的肌肉腱性结构,它将胸腔和腹腔分隔开来。莫尔加尼疝是先天性膈疝(CDH)最罕见的形式,仅占病例的2%至5%。膈疝包括波氏疝、食管裂孔疝和食管旁疝。波氏疝是由于膈肌后外侧区域的缺陷引起的。食管裂孔疝在食管裂孔处有缺陷;食管旁疝在食管裂孔附近有缺陷。莫尔加尼疝起源于胸骨后膈肌前部的缺陷。这种情况比其他类型的先天性膈疝更罕见。由于肺发育不全不常见,莫尔加尼疝往往症状较轻,导致这些缺陷的诊断延迟。

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