Department of Internal Medicine, Wright Center for Graduate Medical Education, Scranton, Pennsylvania, USA.
Department of Internal Medicine, Wright Center for Graduate Medical Education, Scranton, Pennsylvania, USA
BMJ Case Rep. 2020 Jul 16;13(7):e235567. doi: 10.1136/bcr-2020-235567.
Cystic lung disease is a group of heterogeneous pulmonary diseases resulting from hereditary/congenital disorders, systemic disorders and infectious causes among others. Pulmonary mucinous cystic neoplasia is a spectrum of neoplastic cystic diseases with abundant mucin, of which pulmonary mucinous cystadenocarcinoma (PMC) is a rare malignant subtype. We present a case of a 66-year-old man who presented with dyspnoea, cough, fatigue and weight loss. Imaging of his chest showed numerous cavitary lesions, and the diagnosis of PMC was made based on lung biopsy. He received palliative chemotherapy and died 1 year later. We present a literature review of PMC based on 26 reported cases, including our own.
肺囊性疾病是一组异质性肺部疾病,其病因包括遗传/先天性疾病、系统性疾病和感染等。肺黏液囊性肿瘤是一种以大量黏液为特征的囊性肿瘤疾病谱,其中肺黏液囊腺癌(PMC)是一种罕见的恶性亚型。我们报告了一例 66 岁男性患者,其表现为呼吸困难、咳嗽、乏力和体重减轻。胸部影像学检查显示存在多个空洞性病变,肺活检诊断为 PMC。患者接受姑息化疗,1 年后死亡。我们对基于 26 例报告病例(包括我们自己的病例)的 PMC 进行了文献复习。