Chu Patricia Y, Burks Margaret L, Sólorzano Carmen C, Bao Shichun
Department of Internal Medicine, Vanderbilt University Medical Center, Nashville, Tennessee.
Division of Endocrinology, Department of Internal Medicine, Vanderbilt University, Nashville, Tennessee.
AACE Clin Case Rep. 2020 May 4;6(5):e197-e200. doi: 10.4158/ACCR-2019-0558. eCollection 2020 Sep-Oct.
Functional paragangliomas in pregnancy are rare; however, if not recognized and treated early, they can be life-threatening. New treatment approaches with robotic resection are promising.
We present a case of a pregnant female with a paraganglioma which was successfully resected during the second trimester using Da Vinci Xi robotic system. Paraganglioma was diagnosed with plasma and urinary catecholamines and metanephrines, a contrast computed tomography (CT) scan, and confirmed with surgical pathology.
The patient was initially seen in the emergency room prior to the index pregnancy for nausea, vomiting, and intermittent, left lower quadrant abdominal pain, episodic sweating, palpitations, and anxiety. CT scan of the abdomen and pelvis showed a 4.8 × 4.3 cm heterogeneously enhancing mass in the left retroperitoneum adjacent to the aorta just below the left adrenal gland. She had normal plasma metanephrines but elevated plasma normetanephrines of 7.12 nmol/L (normal, <0.89 nmol/L). Twenty-four-hour urine norepinephrine and catecholamines were elevated to 604 μg (normal, <90 μg/24 hours) and 610 μg (normal, <115 μg/24 hours), respectively. Chromogranin A was elevated to 940 ng/mL (normal, 0 to 95 ng/mL). Paraganglioma was suspected. Doxazosin was started for blood pressure control. The patient became pregnant unexpectedly shortly after. She was managed by a multidisciplinary team. At 18 weeks of pregnancy, she underwent a transabdominal robotic resection of the left retroperitoneal paraganglioma with an excellent outcome.
Functional paragangliomas in pregnancy are rare but must be recognized and treated early to reduce maternal and fetal complications. An innovative robotic approach should be considered and explored.
妊娠期功能性副神经节瘤较为罕见;然而,如果未能早期识别和治疗,可能会危及生命。采用机器人切除术的新治疗方法前景广阔。
我们报告一例妊娠期女性副神经节瘤病例,该患者在孕中期使用达芬奇Xi机器人系统成功切除肿瘤。通过检测血浆和尿儿茶酚胺及甲氧基肾上腺素、对比计算机断层扫描(CT)确诊副神经节瘤,并经手术病理证实。
该患者在本次妊娠前因恶心、呕吐、左下腹间歇性腹痛、阵发性出汗、心悸和焦虑首次就诊于急诊室。腹部和盆腔CT扫描显示左肾上腺下方紧邻主动脉的左腹膜后有一个4.8×4.3 cm的不均匀强化肿块。她的血浆甲氧基肾上腺素正常,但血浆去甲氧基肾上腺素升高至7.12 nmol/L(正常,<0.89 nmol/L)。24小时尿去甲肾上腺素和儿茶酚胺分别升高至604 μg(正常,<90 μg/24小时)和610 μg(正常,<115 μg/24小时)。嗜铬粒蛋白A升高至940 ng/mL(正常,0至95 ng/mL)。怀疑为副神经节瘤。开始使用多沙唑嗪控制血压。此后不久患者意外怀孕。由多学科团队进行管理。妊娠18周时,她接受了经腹机器人切除左腹膜后副神经节瘤手术,效果良好。
妊娠期功能性副神经节瘤罕见,但必须早期识别和治疗以减少母婴并发症。应考虑并探索创新的机器人手术方法。