Rauber K, Riemann H
Digitale Bilddiagn. 1987 Jun;7(2):90-3.
Marfan's syndrome is a rare inborn error of metabolism. Marfan patients are prone to aneurysms of the ascending aorta and run a high risk of rupture of the aortic arch. The diameter of the aneurysm is the most important predictor of the risk and therefore the leading point for surgical interventions. IV and IA-DSA according to our experiences are simple and effective methods in pre- and postoperative evaluation of patients with the syndrome.
马方综合征是一种罕见的先天性代谢紊乱疾病。马方综合征患者易患升主动脉瘤,且主动脉弓破裂风险很高。动脉瘤直径是风险的最重要预测指标,因此也是手术干预的关键因素。根据我们的经验,静脉内和动脉内数字减影血管造影(IV和IA-DSA)是该综合征患者术前和术后评估的简单有效方法。