Paediatrician, Department of Pediatrics, Nananvati Hospital, Mumbai, India.
Resident, Department of Pediatrics, B J Wadia Hospital for Children, Mumbai, India.
Trop Doct. 2021 Apr;51(2):271-274. doi: 10.1177/0049475520982694. Epub 2021 Jan 6.
Osteogenesis imperfecta is characterised by low bone mineral density, bone fragility, fractures and deformity. We present five such children treated with intravenous pamidronate, which resulted in a decrease of fracture rate and increase in spinal bone mineral density.
成骨不全症的特征是骨密度低、骨骼脆弱、骨折和畸形。我们介绍了五例接受帕米膦酸钠静脉治疗的此类患儿,结果骨折发生率降低,脊柱骨密度增加。