Wilhelm Raphael, Eckes Timon, Imre Gergely, Kippenberger Stefan, Meissner Markus, Thomas Dominique, Trautmann Sandra, Merlio Jean-Philippe, Chevret Edith, Kaufmann Roland, Pfeilschifter Josef, Koch Alexander, Jäger Manuel
Department of General Pharmacology and Toxicology, Goethe University Hospital and Goethe University Frankfurt, 60590 Frankfurt am Main, Germany.
Department of Dermatology, Venerology and Allergology, Goethe University Hospital, 60590 Frankfurt am Main, Germany.
Cancers (Basel). 2021 Jan 13;13(2):270. doi: 10.3390/cancers13020270.
Cutaneous T cell lymphomas (CTCLs) represent a heterogeneous group of T cell lymphomas that primarily affect the skin. The most frequent forms of CTCL are mycosis fungoides and Sézary syndrome. Both are characterized by frequent recurrence, developing chronic conditions and high mortality with a lack of a curative treatment. In this study, we evaluated the effect of short-chain, cell-permeable C6 Ceramide (C6Cer) on CTCL cell lines and keratinocytes. C6Cer significantly reduced cell viability of CTCL cell lines and induced cell death via apoptosis and necrosis. In contrast, primary human keratinocytes and HaCaT keratinocytes were less affected by C6Cer. Both keratinocyte cell lines showed higher expressions of ceramide catabolizing enzymes and HaCaT keratinocytes were able to metabolize C6Cer faster and more efficiently than CTCL cell lines, which might explain the observed protective effects. Along with other existing skin-directed therapies, C6Cer could be a novel well-tolerated drug for the topical treatment of CTCL.
皮肤T细胞淋巴瘤(CTCL)是一组异质性的T细胞淋巴瘤,主要累及皮肤。CTCL最常见的形式是蕈样肉芽肿和 Sézary 综合征。两者的特点都是频繁复发、发展为慢性病且死亡率高,缺乏治愈性治疗方法。在本研究中,我们评估了短链、可穿透细胞的C6神经酰胺(C6Cer)对CTCL细胞系和角质形成细胞的影响。C6Cer显著降低了CTCL细胞系的细胞活力,并通过凋亡和坏死诱导细胞死亡。相比之下,原代人角质形成细胞和HaCaT角质形成细胞受C6Cer的影响较小。两种角质形成细胞系都显示出神经酰胺分解酶的高表达,并且HaCaT角质形成细胞比CTCL细胞系能够更快、更有效地代谢C6Cer,这可能解释了观察到的保护作用。与其他现有的皮肤定向治疗方法一起,C6Cer可能是一种新型的耐受性良好的药物,用于CTCL的局部治疗。