Department of Radiology, Tianjin Medical University Cancer Institute and Hospital, National Clinical Research Center for Cancer, Key Laboratory of Cancer Prevention and Therapy, Tianjin's Clinical Research Center for Cancer, Tianjin, 300060, China.
J Nucl Cardiol. 2022 Oct;29(5):2734-2737. doi: 10.1007/s12350-020-02470-0. Epub 2021 Feb 8.
Primary pericardial angiosarcoma is a rare malignant cardiac neoplasm with early metastasis and poor prognosis. There are currently no guidelines or effective therapeutic strategies. Here we report a case of a 22-year-old man who presented with chest pain, suffocation and transient syncope over the course of 4 months. Further workup showed a large mass in the right pericardium, histopathologic examination revealed angiosarcoma. The patient subsequently received a total of 8 cycles of chemotherapy (paclitaxel and doxorubicin). This patient has an overall survival of 1 year to date. The current examination methods and reported cases revealed that early detection of primary pericardial angiosarcoma with imaging examinations is critical for prognosis.
原发性心脏血管肉瘤是一种罕见的恶性心脏肿瘤,具有早期转移和预后不良的特点。目前尚无指南或有效的治疗策略。我们在此报告一例 22 岁男性患者,其在 4 个月的病程中出现胸痛、呼吸困难和短暂晕厥。进一步检查显示右心包内有一个大肿块,组织病理学检查显示为血管肉瘤。随后,该患者接受了总共 8 个周期的化疗(紫杉醇和多柔比星)。截至目前,该患者的总生存时间为 1 年。目前的检查方法和已报道的病例表明,早期通过影像学检查发现原发性心脏血管肉瘤对预后至关重要。