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嗜铬细胞瘤危象合并心源性休克时的挽救生命的急诊肾上腺切除术

Life-Saving Emergency Adrenalectomy in a Pheochromocytoma Crisis with Cardiogenic Shock.

作者信息

Bekelaar Thalia, Nougon Gervais, Peters Marc, De Roeck Frederic, Haine Steven, Ysebaert Dirk, Spinhoven Maarten, Jorens Philippe G, De Paep Rudi, Lahaye Frederik

机构信息

Department of Cardiology, Antwerp University Hospital, University of Antwerp, Edegem, Belgium.

Department of Emergency Medicine, Sint-Jozef Hospital, Malle, Belgium.

出版信息

Case Rep Cardiol. 2021 Mar 18;2021:8848893. doi: 10.1155/2021/8848893. eCollection 2021.

Abstract

Cardiogenic shock during a pheochromocytoma crisis is a life-threatening disorder. This case report illustrates a 49-year-old male with profound cardiogenic shock, extreme hemodynamic instability (systolic blood pressure ranging from 45 up to 290 mmHg in a cyclic pattern), and progressive multiple organ failure in the presence of a unilateral adrenal mass. Emergency adrenalectomy led to rapid hemodynamic stabilization. Histological investigation confirmed the diagnosis of pheochromocytoma. This case indicates that emergency adrenalectomy, although usually not considered first choice, is a valid option in cardiogenic shock and extremely fluctuating hemodynamics due to a pheochromcytoma-induced catecholamine storm.

摘要

嗜铬细胞瘤危象期间的心源性休克是一种危及生命的疾病。本病例报告描述了一名49岁男性,患有严重的心源性休克、极度血流动力学不稳定(收缩压呈周期性波动,范围从45至290 mmHg)以及在存在单侧肾上腺肿块的情况下出现进行性多器官功能衰竭。急诊肾上腺切除术导致血流动力学迅速稳定。组织学检查确诊为嗜铬细胞瘤。该病例表明,急诊肾上腺切除术虽然通常不被视为首选,但对于因嗜铬细胞瘤诱发的儿茶酚胺风暴导致的心源性休克和极度波动的血流动力学而言,是一种有效的选择。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f05a/7996044/42f4d878100a/CRIC2021-8848893.001.jpg

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