Daly H M, Haddon M E
Department of Haematology, Bristol Royal Infirmary, UK.
Thromb Haemost. 1988 Apr 8;59(2):171-4.
A three-day-old infant presented with umbilical haemorrhage. Factor XIII deficiency was diagnosed. When one month old she commenced prophylactic injections of pasteurised factor XIII concentrate of human plasma origin. During two and a half years treatment there were no haemorrhagic episodes and factor XIII concentrate was well tolerated. Satisfactory post infusion factor XIII levels were achieved. Three transient elevations of aspartate transaminase occurred, the cause of which has not been established. There was no evidence of transmission of hepatitis or H.I.V. infection. A brother, born one year later, is also affected and commenced prophylactic therapy with the same factor XIII concentrate. Experience in these two infants suggests the product is efficacious.
一名三日龄婴儿出现脐部出血。诊断为因子 XIII 缺乏症。在其一个月大时开始预防性注射人血浆来源的巴氏消毒因子 XIII 浓缩物。在两年半的治疗期间未发生出血事件,且因子 XIII 浓缩物耐受性良好。输注后因子 XIII 水平达到令人满意的程度。天冬氨酸转氨酶出现三次短暂升高,其原因尚未明确。没有肝炎或艾滋病毒感染传播的证据。一年后出生的一个弟弟也受到影响,并开始使用相同的因子 XIII 浓缩物进行预防性治疗。这两名婴儿的治疗经验表明该产品有效。