Department of Head and Neck Surgery & Communication Sciences, Duke University, Durham, North Carolina.
Otol Neurotol. 2021 Sep 1;42(8):e1062-e1066. doi: 10.1097/MAO.0000000000003218.
Inflammatory pseudotumor of the temporal bone is a benign idiopathic inflammatory process that is rarely encountered in clinical practice. We describe a novel case of a patient who developed superior semicircular canal dehiscence syndrome in the setting of active inflammatory pseudotumor of the temporal bone.
One female patient found to have inflammatory pseudotumor of the temporal bone. After treatment with mastoidectomy and steroids, she subsequently developed superior semicircular canal dehiscence syndrome.
The patient initially underwent myringotomy and pressure equalization tube placement for a unilateral effusion. Imaging with computed tomography and magnetic resonance imaging revealed a lytic mastoid mass. A complete mastoidectomy was diagnostic for inflammatory pseudotumor and the patient was treated with adjuvant long-term corticosteroids. After this procedure, she was discovered to have new development of symptomatic superior semicircular canal dehiscence syndrome. She eventually underwent a trans-mastoid repair of her superior semicircular canal dehiscence.
The patient's clinical course is described with emphasis on the development of superior semicircular canal dehiscence syndrome in the setting of active inflammatory pseudotumor of the temporal bone.
The patient's radiographic and clinical history were found to be consistent with inflammatory pseudotumor of the temporal bone. She underwent a therapeutic mastoidectomy with long-term post-operative corticosteroids. During her post-operative course, she developed symptoms of vertigo, hearing loss, and autophony. She was subsequently diagnosed with superior semicircular canal dehiscence and treated with a trans-mastoid repair of the dehiscence. Her symptoms satisfactorily resolved after this surgery.
Inflammatory pseudotumor of the temporal bone is a rare benign inflammatory process. We present what is to our knowledge the first description of superior semicircular canal dehiscence syndrome developing in the setting of inflammatory pseudotumor.
颞骨炎性假瘤是一种罕见的临床良性特发性炎症过程。我们描述了一例新的患者,其在颞骨炎性假瘤活动期发生了上半规管裂综合征。
一位女性患者被发现患有颞骨炎性假瘤。在接受乳突切除术和类固醇治疗后,她随后出现了上半规管裂综合征。
患者最初因单侧积液行鼓膜切开和压力平衡管放置。计算机断层扫描和磁共振成像显示出溶骨性乳突肿块。完整的乳突切除术被诊断为炎性假瘤,患者接受了辅助长期皮质类固醇治疗。在此手术后,她被发现出现新的症状性上半规管裂综合征。最终,她接受了上半规管裂经乳突修复术。
描述患者的临床病程,重点是在上半规管裂综合征活动期的颞骨炎性假瘤背景下的发展。
患者的影像学和临床病史与颞骨炎性假瘤相符。她接受了治疗性乳突切除术,并长期接受术后皮质类固醇治疗。在术后过程中,她出现了眩晕、听力损失和自声现象的症状。随后被诊断为上半规管裂,并接受了经乳突修复术。手术后,她的症状得到了满意的缓解。
颞骨炎性假瘤是一种罕见的良性炎症过程。我们提出了迄今为止关于上半规管裂综合征在炎性假瘤背景下发展的首例描述。