Ortega-Zhindón Diego B, Flores-Sarria Iris P, Minakata-Quiróga María A, Angulo-Cruzado Stephanie T, Romero-Montalvo Luis A, Cervantes-Salazar Jorge L
Departamento de Cirugía Cardiaca Pediátrica y Cardiopatías Congénitas, Instituto Nacional de Cardiología Ignacio Chávez, Ciudad de México, México.
Departamento de Anestesia Cardiovascular, Instituto Nacional de Cardiología Ignacio Chávez, Ciudad de México, México.
Arch Cardiol Mex. 2021 Nov 1;91(4):470-479. doi: 10.24875/ACM.20000567.
Atrial isomerism describes complex anatomical findings with defects in the determination of lateralization; being a rare situation, with a prevalence of 1 in every 10.000 to 20.000 live births, with an incidence of up to 4% of all cardiac malformations. The diagnosis can be made in the neonatal age; however, clinical presentation is nonspecific. Depending on the spectrum of malformations, complex and invasive diagnostic tools may be required. Treatment is varied and can range from palliative surgery in view of univentricular physiology to total correction surgery for biventricular repair.
心房异构描述了在确定左右侧化方面存在缺陷的复杂解剖学发现；这是一种罕见情况，在每10000至20000例活产中发生率为1，占所有心脏畸形的比例高达4%。该诊断可在新生儿期做出；然而，临床表现并无特异性。根据畸形的范围，可能需要复杂且侵入性的诊断工具。治疗方法多样，从针对单心室生理状况的姑息性手术到双心室修复的完全矫正手术不等。
