Servicio de Anestesiología y Reanimación, Hospital Clínico Universitario de Valladolid, Valladolid, Spain.
Servicio de Anestesiología y Reanimación, Hospital de Medina del Campo, Medina del Campo, Valladolid, Spain.
Rev Esp Anestesiol Reanim (Engl Ed). 2021 Nov;68(9):537-541. doi: 10.1016/j.redare.2020.08.014. Epub 2021 Nov 4.
Kartagener's syndrome (KS) is a rare genetic disease characterised by the triad of sinusitis, bronchiectasis, and situs inversus. This syndrome is associated with an increased risk of respiratory complications. Therefore, both the anaesthetic technique and the agents used must be carefully chosen according to the type of intervention and the patient's baseline condition. We present the case of a 48-year-old woman with KS, scheduled for functional endoscopic sinus surgery (FESS) and septoplasty under general anaesthesia. The main anaesthetic considerations in patients with KS are related to anatomical variations, pulmonary and cardiac functions, and respiratory infections. In this case, measures that reduce perioperative complications in KS are reviewed together with the special anaesthetic management in FESS, derived primarily from the need to maintain a bloodless surgical field and the use of induced hypotension techniques.
卡塔格内氏综合征（KS）是一种罕见的遗传性疾病，其特征为三联征，即鼻窦炎、支气管扩张和内脏转位。该综合征与呼吸道并发症的风险增加有关。因此，麻醉技术和所用药物必须根据干预类型和患者的基线情况仔细选择。我们介绍了一例 48 岁的 KS 女性患者，拟在全身麻醉下接受功能性内窥镜鼻窦手术（FESS）和鼻中隔成形术。KS 患者的主要麻醉注意事项与解剖变异、肺和心脏功能以及呼吸道感染有关。在这种情况下，我们一起审查了可降低 KS 围手术期并发症的措施，以及 FESS 中的特殊麻醉管理，主要源于需要保持无血手术视野和使用诱导性低血压技术。
