Pars plana technique for removal of congenital subluxated lenses in young patients.

Lensectomy with the pars plana technique was performed in 16 eyes of 11 patients (2 female, 9 male) with congenital subluxated lenses. Lens subluxation was associated with homocystinuria in 2 patients, Marfan's syndrome in 4, congenital simple ectopia lentis in 2 and without any known heredity in 3 patients. The reason for removal was in all eyes optical disturbances. Five patients were operated on both eyes. All lenses were removed with the Kløti Vitreous Stripper through the pars plana. No complications occurred. Retinal detachment was present pre-operatively in both eyes in one patient with homocystinuria. In the post-operative period, prophylactic photocoagulation and cryotherapy were performed in 7 eyes in 6 patients (6 photocoagulation and 1 cryo). The pars plana technique for removal of clear subluxated lenses in young individuals seems to be the method of choice. Complications are negligible and the method gives excellent optical results.