Raja Anand, Malik Kanuj, Mahalingam Sivakumar
Department of Surgical Oncology, Cancer Institute (WIA), Chennai, Tamil Nadu, India.
Department of Surgical Oncology, Fortis Malar Hospital, Chennai, Tamil Nadu, India.
J Indian Assoc Pediatr Surg. 2022 Jan-Feb;27(1):109-111. doi: 10.4103/jiaps.JIAPS_282_20. Epub 2022 Jan 11.
Castleman's disease is a rare lymphoproliferative disorder of poorly understood etiology. It is most commonly located in the mediastinum. Castleman's disease mimicking adrenal neoplasm is a very rare differential diagnosis and unusual presentation. We report a rare suprarenal unicentric hyaline vascular variant of the disease in a 16-year-old boy with atypical symptoms mimicking an adrenal neoplasm.
卡斯特曼病是一种病因不明的罕见淋巴增生性疾病。它最常位于纵隔。酷似肾上腺肿瘤的卡斯特曼病是一种非常罕见的鉴别诊断和不寻常表现。我们报告了一名16岁男孩患有一种罕见的肾上腺单中心透明血管型卡斯特曼病,其具有酷似肾上腺肿瘤的非典型症状。