Int J Clin Pharmacol Ther. 2022 Jul;60(7):311-316. doi: 10.5414/CP204190.
Hereditary transthyretin amyloidosis (hATTR) is an ultra-rare illness. Inotersen is a 2'-O-methoxyethyl (2'MOE)-modified antisense oligonucleotides (ASO) approved in 2018 as a polyneuropathy treatment for adults with hereditary transthyretin amyloidosis stages 1 or 2. Inotersen can produce grade 4 thrombocytopenia as a severe adverse reaction that can lead to potentially fatal hemorrhage complications. We describe our experience in the management of severe thrombocytopenia with inotersen. The onset of the thrombocytopenia and the incidences described in the cases in our hospital are different from that described in the literature. Also, recovery of platelet levels was faster in our patient who was administered human immunoglobulin G, which suggests that there is an immunological component.
遗传性转甲状腺素蛋白淀粉样变性(hATTR)是一种超罕见疾病。Inotersen 是一种 2'-O-甲氧基乙基(2'MOE)修饰的反义寡核苷酸(ASO),于 2018 年获批用于治疗遗传性转甲状腺素蛋白淀粉样变性 1 或 2 期的成人多发性神经病。Inotersen 可引起血小板减少症 4 级等严重不良反应,从而导致潜在致命的出血并发症。我们描述了使用 Inotersen 治疗严重血小板减少症的经验。我们医院所描述的血小板减少症的发病和发生率与文献中的描述不同。此外,接受人免疫球蛋白 G 治疗的患者血小板计数恢复更快,这表明存在免疫成分。