Yam Max K H, Chan Kenneth K K
Department of Radiology, North District Hospital, 9 Po Kin Road, Sheung shui, the New Territories, Hong Kong.
Radiol Case Rep. 2022 Apr 5;17(6):1938-1941. doi: 10.1016/j.radcr.2022.02.076. eCollection 2022 Jun.
Alveolar soft part sarcoma (ASPS) is a rare, highly vascular, deep soft tissue mesenchymal malignancy that is classically seen in the lower extremities of young adults. We reported a case of a 32-year-old young Chinese woman in Hong Kong with a biopsy-proven alveolar soft part sarcoma. The condition can be suggested by classical features using contrast-enhanced CT scans and MRIs or confirmed by image-guided biopsies. Early recognition of the condition is important due to its poor prognosis and lack of awareness. The mainstay of treatment for ASPS is complete surgical resection of the primary tumor and radiotherapy for microscopic residual disease at the primary site, or chemotherapy in special cases.
肺泡软组织肉瘤(ASPS)是一种罕见的、血管丰富的深部软组织间叶恶性肿瘤,典型表现于年轻成人的下肢。我们报告了一例32岁的中国香港年轻女性病例,经活检证实为肺泡软组织肉瘤。通过增强CT扫描和MRI的典型特征可提示该病,或通过影像引导下活检确诊。由于其预后较差且认知不足,早期识别该病很重要。ASPS的主要治疗方法是完整手术切除原发肿瘤,对原发部位的微小残留病灶进行放疗,特殊情况下进行化疗。