Hematian Mohammad Nasir, Torabi Shirin, Hantoushzadeh Sedigheh, Dehestani Alireza, Dadkhah Minoo, Shabanian Reza
Department of Pediatric Cardiology, Yas Hospital Complex, Tehran University of Medical Sciences, Tehran, Iran.
Department of Obstetrics and Gynecology, Vali-Asr Hospital, Tehran University of Medical Sciences, Tehran, Iran.
Egypt Heart J. 2022 Apr 11;74(1):26. doi: 10.1186/s43044-022-00263-z.
Accessory mitral valve tissue (AMVT) is a rare congenital cardiac anomaly that mainly diagnosed in the first decade of life. However, asymptomatic cases may not be diagnosed even up to adulthood. We report a fetus with AMVT to show the diagnostic ability of the fetal echocardiography for detection of this pathology in the prenatal period.
AMVT was diagnosed in a 26-week-old male fetus with persistent dysrhythmia. Dysrhythmia could not be aborted and controlled by sotalol till the third trimester evaluation. Apical left ventricular (LV) diverticulum was the additional finding in his fetal echocardiogram. After birth, he was in sinus rhythm and echocardiography confirmed the presence of AMVT, however, without any evidence of LV apical diverticulum.
The diagnosis of AMVT in the prenatal period is possible by fetal echocardiography.
二尖瓣附属组织（AMVT）是一种罕见的先天性心脏异常，主要在生命的第一个十年被诊断出来。然而，无症状的病例甚至到成年期都可能未被诊断出来。我们报告一例患有AMVT的胎儿，以展示胎儿超声心动图在产前检测这种病变的诊断能力。
一名患有持续性心律失常的26周龄男性胎儿被诊断为AMVT。直到孕晚期评估时，索他洛尔都无法终止和控制心律失常。胎儿超声心动图的额外发现是左心室心尖憩室。出生后，他处于窦性心律，超声心动图证实存在AMVT，但没有任何左心室心尖憩室的证据。
通过胎儿超声心动图在产前诊断AMVT是可能的。
