Center for Benign Haematology, Thrombosis and Haemostasis, Van Creveldkliniek, University Medical Center Utrecht, Utrecht University, Utrecht, The Netherlands.
Department of Hematology, HagaZiekenhuis, The Hague, The Netherlands.
Am J Hematol. 2022 Jul;97(7):924-932. doi: 10.1002/ajh.26581. Epub 2022 May 10.
Iron overload is a severe general complication of hereditary anemias. Treatment with iron chelators is hampered by important side-effects, high costs, and the lack of availability in many countries with a high prevalence of hereditary anemias. In this phase III randomized placebo-controlled trial, we assigned adults with non-transfusion-dependent hereditary anemias with mild-to-moderate iron overload to receive esomeprazole (at a dose of 40 mg twice daily) or placebo for 12 months in a cross-over design. The primary end point was change of liver iron content measured by MRI. A total of 30 participants were enrolled in the trial. Treatment with esomeprazole resulted in a statistically significant reduction in liver iron content that was 0.55 mg Fe/g dw larger than after treatment with placebo (95%CI [0.05 to 1.06]; p = 0.03). Median baseline liver iron content at the start of esomeprazole was 4.99 versus 4.49 mg Fe/g dw at start of placebo. Mean delta liver iron content after esomeprazole treatment was -0.57 (SD 1.20) versus -0.11 mg Fe/g dw (SD 0.75) after placebo treatment. Esomeprazole was well tolerated, reported adverse events were mild and none of the patients withdrew from the study due to side effects. In summary, esomeprazole resulted in a significant reduction in liver iron content when compared to placebo in a heterogeneous group of patients with non-transfusion-dependent hereditary anemias. From an international perspective this result can have major implications given the fact that proton pump inhibitors may frequently be the only realistic therapy for many patients without access to or not tolerating iron chelators.
铁过载是遗传性贫血的一种严重的全身性并发症。铁螯合剂的治疗受到严重副作用、高成本以及在遗传性贫血高发的许多国家缺乏可用性的限制。在这项 III 期随机安慰剂对照试验中,我们将非输血依赖型遗传性贫血且铁过载程度为轻度至中度的成年人按交叉设计分为两组,一组接受埃索美拉唑(剂量为 40mg,每日两次)治疗,另一组接受安慰剂治疗,疗程为 12 个月。主要终点是通过 MRI 测量肝脏铁含量的变化。共有 30 名参与者入组该试验。与安慰剂治疗相比,埃索美拉唑治疗可使肝脏铁含量显著降低,差值为 0.55mg Fe/g dw(95%CI [0.05 至 1.06];p = 0.03)。埃索美拉唑治疗开始时的中位基线肝脏铁含量为 4.99mg Fe/g dw,安慰剂治疗开始时的中位基线肝脏铁含量为 4.49mg Fe/g dw。埃索美拉唑治疗后的平均肝脏铁含量差值为 -0.57(SD 1.20)mg Fe/g dw,安慰剂治疗后的平均肝脏铁含量差值为 -0.11mg Fe/g dw(SD 0.75)。埃索美拉唑耐受性良好,报告的不良事件轻微,没有患者因副作用退出研究。总之,与安慰剂相比,埃索美拉唑可显著降低非输血依赖型遗传性贫血患者肝脏铁含量。从国际角度来看,鉴于质子泵抑制剂可能经常是许多无法获得或不能耐受铁螯合剂的患者唯一可行的治疗方法,这一结果具有重要意义。