Cross-sectional and pulsed Doppler echocardiography of the atrioventricular junction of hearts with univentricular atrioventricular connexion.

The atrioventricular junction of 52 consecutive patients with univentricular atrioventricular connexion was examined by cross-sectional and pulsed Doppler echocardiography. The echocardiographic features were then compared with catheterisation and cineangiographic findings. In the diagnosis of the mode of atrioventricular connexion, cross-sectional echocardiography was superior to cineangiography in differentiating single inlet with absence of one atrioventricular connexion from double inlet with a common atrioventricular valve. Straddling atrioventricular valves were diagnosed by echocardiography alone. Using pulsed Doppler echocardiography, the diagnostic sensitivity of atrioventricular valvar regurgitation was 92.6% and the specificity 100%. By mapping the regurgitant jet with pulsed Doppler echocardiography, an index was derived to evaluate the severity of atrioventricular valvar regurgitation. The indices obtained correlated well with cineangiographic grading on a three-point scale (Spearman rank correlation coefficient: rs = 0.9). Thus, cross-sectional echocardiography coupled with a range-gated Doppler system provide accurate anatomical details of the atrioventricular junction and reliable assessment of atrioventricular valvar regurgitation in patients with univentricular atrioventricular connexion.