Division of Hepatobiliary Pancreatic Surgery and Transplantation, Department of Surgery, Graduate School of Medicine Kyoto University, Kyoto, Japan.
Division of Hepatobiliary Pancreatic Surgery and Transplantation, Department of Surgery, Graduate School of Medicine Kyoto University, Kyoto, Japan.
Surg Oncol. 2022 Aug;43:101815. doi: 10.1016/j.suronc.2022.101815. Epub 2022 Jul 8.
Situs inversus totalis (SIT) is a rare congenital condition characterized by complete transposition (right-to-left reversal) of the thoracic and abdominal organs. The estimated prevalence of SIT is 1 per 8000-25,000 live births [1]. Surgery for abdominal diseases in patients with SIT is technically demanding because of anatomical variations [2-4]; the importance of preoperative radiological assessment has been reported [4]. We report a case of SIT with complex vascular anomalies and pancreatic body cancer who underwent pancreatoduodenectomy with combined resection of the portal vein.
A 79-year-old man with asymptomatic SIT was referred to our hospital for the treatment of pancreatic cancer that was incidentally found during a medical check-up. Abdominal computed tomography (CT) revealed a hypovascular tumor in the pancreatic body with a diameter of 32 mm involving the portal vein. He did not have SIT-associated diseases such as Kartagener syndrome or other malformations but had complex anomalies of vascular anatomy, especially in the hepatic arterial system, in addition to mirror-image transposition.
The operation was performed successfully with a full understanding of the vascular anatomy based on precise preoperative evaluation of CT images, including three-dimensional reconstruction images. The operative time was 710 min, and blood loss was 1237 mL. The Union for International Cancer Control (UICC) pathological stage was Stage III (T2, N2, M0).
Pancreatoduodenectomy with portal vein resection for pancreatic cancer in patients with SIT is a complex procedure. Precise preoperative assessment of CT images with three-dimensional reconstruction is crucial to understanding vascular anatomy and safely performing surgery.
全内脏反位(SIT)是一种罕见的先天性疾病,其特征为胸腔和腹腔器官完全转位(左右反转)。SIT 的估计患病率为每 8000-25000 例活产儿中 1 例[1]。由于解剖结构的变异,SIT 患者的腹部疾病手术具有很高的技术要求[2-4];术前影像学评估的重要性已被报道[4]。我们报告了一例 SIT 合并复杂血管异常和胰体癌患者,行胰十二指肠切除术联合门静脉切除。
一名 79 岁无症状 SIT 男性患者因体检时偶然发现胰体部占位性病变而被转诊至我院。腹部 CT 显示胰体部有一 32mm 直径的低血供肿瘤,累及门静脉。患者无 Kartagener 综合征或其他畸形等 SIT 相关疾病,但除镜像反转外,还存在复杂的血管解剖学异常,特别是肝动脉系统。
根据 CT 图像,包括三维重建图像的精确术前评估,充分了解血管解剖结构后,手术顺利进行。手术时间为 710 分钟,出血量为 1237ml。国际抗癌联盟(UICC)病理分期为 III 期(T2,N2,M0)。
SIT 患者胰体癌胰十二指肠切除术联合门静脉切除是一项复杂的手术。术前通过 CT 图像的三维重建进行精确评估对于理解血管解剖结构和安全手术至关重要。