Cerrahpasa Medical Faculty, Department of Internal Medicine, Istanbul University-Cerrahpasa, Istanbul, Turkey.
Dermatol Ther. 2022 Nov;35(11):e15785. doi: 10.1111/dth.15785. Epub 2022 Sep 8.
Drug reaction with eosinophilia and systemic symptoms (DRESS) syndrome is an uncommon systemic adverse drug reaction. Furthermore, it is a unique syndrome encompassing various manifestations of fever, facial edema, eosinophilia, atypical lymphocytosis, and organ dysfunction. Since there are no large prospective studies concerning DRESS syndrome, current treatment modalities for DRESS have been mainly determined based on various case reports and expert opinions. Corticosteroids are the mainstay of therapy after the cessation of the culprit drug. Although most cases recover within a couple of months, some may persist and even progress despite 1 mg/kg/day of prednisolone or its equivalent. We herein present two cases of severe DRESS syndrome. Both cases presented with organ dysfunction and remained unresponsive to initial treatment with 1 mg/kg/day of intravenous methylprednisolone. Therefore, plasmapheresis or pulse steroid therapy (250 mg/day methylprednisolone for 3 days) was used. In the follow-up period, the patients' clinical conditions improved dramatically without recurrence. We aimed to share our experience in recognizing and managing severe DRESS cases in this manuscript. Furthermore, we reviewed the literature in comparison with the present cases. In conclusion, plasmapheresis or pulse steroid therapy (250 mg/day of methylprednisolone for 3 days) can be used to treat difficult DRESS cases where organ failure is about to happen.
药物反应伴嗜酸性粒细胞增多和全身性症状(DRESS)综合征是一种不常见的全身性药物不良反应。此外,它是一种独特的综合征,包括发热、面部水肿、嗜酸性粒细胞增多、非典型淋巴细胞增多和器官功能障碍等各种表现。由于目前尚无关于 DRESS 综合征的大型前瞻性研究,因此 DRESS 的当前治疗方法主要是基于各种病例报告和专家意见确定的。在停用致病药物后,皮质类固醇是治疗的主要方法。尽管大多数病例在几个月内恢复,但有些病例尽管使用了 1mg/kg/天的泼尼松龙或其等效剂量,仍持续存在甚至进展。本文介绍了两例严重的 DRESS 综合征病例。这两例病例均出现器官功能障碍,对初始 1mg/kg/天静脉注射甲基泼尼松龙治疗无反应。因此,采用了血浆置换或脉冲类固醇治疗(250mg/天甲基泼尼松龙,连用 3 天)。在随访期间,患者的临床状况显著改善,无复发。我们旨在通过本文分享我们在识别和管理严重 DRESS 病例方面的经验。此外,我们还对文献进行了回顾,并与本病例进行了比较。总之,在即将发生器官衰竭的情况下,血浆置换或脉冲类固醇治疗(250mg/天甲基泼尼松龙,连用 3 天)可用于治疗棘手的 DRESS 病例。