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孤立性先天性右肺动脉缺如并肺动脉高压伴冠状动脉侧支循环:病例报告。

An isolated congenital absence of right pulmonary artery associated with pulmonary hypertension with coronary collaterals: A case report.

机构信息

Department of Cardiology, Dicle University School of Medicine, Diyarbakir, Turkey.

Department of Cardiology, Memorial Hospital, Diyarbakir, Turkey.

出版信息

Echocardiography. 2022 Oct;39(10):1367-1369. doi: 10.1111/echo.15450. Epub 2022 Sep 13.

Abstract

Unilateral absence of pulmonary artery (UAPA) resulting from a defect in the aortic arch's embryogenesis. Patients who survive into adulthood is rare. Herein, we presented a case of UAPA with pulmonary hypertension in a 49-year old female.

摘要

单侧肺动脉缺如(UAPA)是由于主动脉弓胚胎发育缺陷引起的。成年后存活的患者极为罕见。本文报道了 1 例 49 岁女性合并肺动脉高压的 UAPA 病例。

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