NHS Tayside, UK.
Ann R Coll Surg Engl. 2023 May;105(5):484-488. doi: 10.1308/rcsann.2022.0107. Epub 2022 Oct 14.
Diaphragmatic hernias can be congenital or acquired and are a protrusion of intra-abdominal contents through an abnormal opening in the diaphragm. Acquired defects are rare and occur secondary to direct penetrating injury or blunt abdominal trauma. This case review demonstrates two unconventional cases of large diaphragmatic hernias with viscero-abdominal disproportion in adults. Case 1 is a 27-year-old man with no prior medical or surgical history. He presented following a 24-h history of increasing shortness of breath and left-sided pleuritic chest pain, and no history of trauma. Chest X-ray demonstrated loops of bowel within the left hemithorax with displacement of the mediastinum to the right. Computed tomography (CT) scan confirmed a large diaphragmatic defect causing herniation of most of his abdominal contents into the left hemithorax. He underwent emergency surgery, which confirmed the viscero-abdominal disproportion. He required an extended right hemicolectomy to reduce the volume of the abdominal comtents and laparostomy to reduce the risk of abdominal compartment syndrome and recurrence of the hernia. Case 2 is a 76-year-old man with significant medical comorbidities who presented with acute onset of abdominal pain. He had a history of traumatic right-sided chest injury as a child resulting in right-sided diaphragmatic paralysis. Chest X-ray demonstrated a large right-sided diaphragmatic hernia with abdominal viscera in the right thoracic cavity. CT scan of the chest, abdomen and pelvis demonstrated both small and large bowel loops within the right hemithorax, compression of the right lung and displacement of the mediastinum to the left. The CT scan also demonstarted viscero-abdominal disproportion. Operative management was considered initially but following improvement with basic medical management and no further deterioration, a non-operative approach was adopted. Both cases illustrate atypical presentations of adults with diaphragmatic hernias. In an ideal scenario, these are repaired surgically. When the presumed diagnosis shows characteristics of a viscero-abdominal disproportion and surgery is pursued, the surgeon must consider that primary abdominal closure may not be possible and multiple operations may be necessary to correct the defect and achieve closure. Sacrifice of abdominal viscera may also be necessary to reduce the volume of abdominal contents.
膈疝可分为先天性和后天性,是指腹腔内容物通过膈肌的异常开口疝出。后天性膈疝罕见,继发于直接穿透性损伤或钝性腹部创伤。本病例报告展示了两例成人非典型巨大膈疝伴内脏-腹部比例失调。病例 1 为 27 岁男性,无既往病史。他在出现 24 小时进行性呼吸困难和左侧胸痛后就诊,无外伤史。胸部 X 线片显示左侧胸腔内有肠袢,纵隔向右侧移位。计算机断层扫描(CT)扫描证实存在巨大膈疝,导致大部分腹部内容物疝入左侧胸腔。他接受了紧急手术,证实了内脏-腹部比例失调。他需要进行扩大的右半结肠切除术以减小腹部内容物的体积,并进行剖腹术以降低腹腔间隔室综合征和疝复发的风险。病例 2 为 76 岁男性,有多种严重合并症,因突发腹痛就诊。他在儿童时期曾有右侧胸部创伤史,导致右侧膈肌麻痹。胸部 X 线片显示右侧巨大膈疝,腹部内脏疝入右侧胸腔。胸部、腹部和骨盆 CT 扫描显示右侧胸腔内有小肠和大肠袢,右侧肺受压,纵隔向左侧移位。CT 扫描还显示了内脏-腹部比例失调。最初考虑手术治疗,但在基本医疗管理后病情改善且无进一步恶化后,采用了非手术治疗。这两个病例均展示了成人膈疝的非典型表现。在理想情况下,这些患者需要接受手术治疗。当疑似诊断显示出内脏-腹部比例失调的特征,且需要手术治疗时,外科医生必须考虑到可能无法进行原发性腹部关闭,并且可能需要多次手术来纠正缺陷并实现关闭。为了减小腹部内容物的体积,可能还需要牺牲腹部内脏。