Kalra Rishita, Rizvi Sama, Pathak Vivek Kumar, Nayak Pradeepti
Department of Otorhinolaryngology, School of Medical Sciences and Research, Sharda University, Greater Noida, Uttar Pradesh, India.
Iran J Otorhinolaryngol. 2022 Nov;34(125):319-326. doi: 10.22038/IJORL.2022.64705.3221.
Haemangioma or hemangioendothelioma is amongst the commonest developmental, vascular lesions of infancy and childhood. Hemangioendothelioma of the salivary glands, however, is extremely rare. Due to their rarity, they may be misdiagnosed as lymphangiomas or other cystic lesions found more commonly in the region. This may lead to surgical complications including torrential hemorrhage that may have dire consequences for the patient.
Herein we present the case of a nine-year-old male with a cavernous haemangioma involving the left submandibular gland which was diagnosed on-table due to inconclusive pre-operative radiological and pathological diagnosis. Fortunately, due to meticulous dissection and care the lesion was excised in toto without any significant blood loss.
Haemangioma of the submandibular gland is so uncommon that often it isn't even considered a differential diagnosis for cystic swellings and lesions in this region. Mistaken diagnoses preoperatively may prove disastrous for the patient. Excision of haemangiomas requires planning for hemostasis and blood loss if it occurs. Even minor iatrogenic manipulation of vascular lesions may completely obscure the field due to bleeding, making dissection and recognition of anatomical landmarks very difficult. This is especially dangerous in the submandibular region due to the proximity of various vital vascular and neural elements. A differential of haemangioma should therefore always be considered by surgeons and radiologists alike for lesions with suspicious or indeterminate features, in this region.
血管瘤或血管内皮瘤是婴幼儿期最常见的发育性血管病变。然而,涎腺血管内皮瘤极为罕见。由于其罕见性,它们可能被误诊为淋巴管瘤或该区域更常见的其他囊性病变。这可能导致手术并发症,包括大出血,对患者可能产生严重后果。
在此,我们报告一例9岁男性患者,其左下颌下腺患有海绵状血管瘤,由于术前影像学和病理学诊断不明确,术中得以确诊。幸运的是,由于细致的解剖和小心操作,病变被完整切除,未出现明显失血。
下颌下腺血管瘤非常罕见,以至于在该区域囊性肿胀和病变的鉴别诊断中甚至常常不被考虑。术前误诊可能对患者造成灾难性后果。切除血管瘤需要制定止血计划并应对可能出现的失血情况。即使对血管病变进行轻微的医源性操作,也可能因出血而使术野完全模糊,导致解剖分离和识别解剖标志非常困难。由于下颌下区域靠近各种重要的血管和神经结构,这一点尤其危险。因此,对于该区域具有可疑或不确定特征的病变,外科医生和放射科医生都应始终考虑血管瘤的鉴别诊断。