Parnes L S, McCabe B F
Department of Otolaryngology, Head and Neck Surgery, University of Iowa, Iowa City.
Pediatrics. 1987 Oct;80(4):524-8.
This study underscores the importance of considering a perilymph fistula, an abnormal communication between the inner and middle ear, in any child with a progressive sensorineural hearing loss. A concomitant complaint of intermittent dizziness or observed spells of imbalance (56%) is another indication of the disease. Six of 16 patients (37.5%) with proven fistulas were less than 2 years of age at the onset of symptoms. Unless the fistula is identified and repaired by grafting, the ear may become totally deaf. This would be disastrous in the presence of bilateral fistulas, which occur commonly in children (56% of patients had symptoms of bilateral disease). Our experience in recognizing and treating fistulas and thereby saving and restoring hearing is described.
本研究强调，对于任何患有进行性感音神经性听力损失的儿童，都要考虑到存在外淋巴瘘，即内耳与中耳之间的异常连通。间歇性头晕或观察到的失衡发作（56%）的伴随症状是该疾病的另一个指征。16例经证实患有瘘管的患者中，有6例（37.5%）在症状出现时年龄小于2岁。除非通过移植手术识别并修复瘘管，否则耳朵可能会完全失聪。如果存在双侧瘘管，这将是灾难性的，而双侧瘘管在儿童中很常见（56%的患者有双侧疾病症状）。本文描述了我们在识别和治疗瘘管从而挽救和恢复听力方面的经验。
