右肩胛区性腺外混合性生殖细胞肿瘤 1 例报告。
Extragonadal Mixed Germ Cell Tumour of the Right Scapular Region: A Case Report.
机构信息
Department of Paediatric Hematology and Oncology, Bhaktapur Cancer Hospital, Dudhpati, Bhaktapur, Nepal.
Department of Paediatric Hematology and Oncology, National Institute of Cancer Research and Hospital, Mohakhali, Dhaka, Bangladesh.
出版信息
JNMA J Nepal Med Assoc. 2022 Dec 1;60(256):1052-1055. doi: 10.31729/jnma.7910.
UNLABELLED
Extragonadal germ cell tumours are rare; to the best of our knowledge, a location in the soft tissue of the right scapular region has never been previously reported in the literature. We report a case of a 9-years-old girl who presented with swelling over the right scapular region, treated by a combination of surgery and cisplatin-based chemotherapy. Immunohistochemistry and serum tumour markers concluded it to be an extragonadal mixed germ cell tumour. Our patient had a complete response up to 2 years of follow-up. This case is being reported here due to a very rare site of presentation with a diagnostic dilemma. A multidisciplinary, combining systemic chemotherapy and surgery is the most appropriate treatment strategy for extragonadal germ cell tumours, to ensure both local and systemic control.
KEYWORDS
germ cell tumor; immunohistochemistry; tumor markers.
未注明
生殖细胞肿瘤在性腺外很少见；据我们所知，文献中从未报道过位于右肩胛区软组织的生殖细胞肿瘤。我们报告了一例 9 岁女孩，她因右肩胛区肿胀就诊，采用手术联合顺铂为基础的化疗进行治疗。免疫组化和血清肿瘤标志物检查结果提示为性腺外混合生殖细胞肿瘤。我们的患者在 2 年的随访中完全缓解。由于该病例表现极为罕见，诊断存在一定困难，故在此报告。多学科联合全身化疗和手术是治疗性腺外生殖细胞肿瘤的最恰当策略，可确保局部和全身控制。
关键词
生殖细胞瘤；免疫组化；肿瘤标志物。
Zotero 插件