Benabdallah Wajdi, Othmane Mouna Ben, Bouassida Khaireddine, Hmida Wissem, Jaidane Mehdi
Urology Department, Sahloul Hospital, Sousse, Tunisia.
Urology Department, Sahloul Hospital, Sousse, Tunisia.
Int J Surg Case Rep. 2023 May;106:108218. doi: 10.1016/j.ijscr.2023.108218. Epub 2023 Apr 17.
Crossed fused renal ectopia is a rare congenital anomaly characterized by both kidneys being fused together on one side of the spine. Herein, we present an atypical subtype of this disease. To our best knowledge, in the current literature, there is few cases reported with superior crossed fused renal ectopia of the right kidney.
A 40-year-old man with diabetes type 1 presented to our hospital with diabetic ketoacidosis and abdominal pain initially taken care of in an endocrinology department then transferred to our urology department after discovery on the CT scan of a staghorn calculus in the solitary right kidney is later discovered during the therapeutic management that it is a superior CFRE.
Unilateral fused renal superior ectopia is extremely rare and the management of urinary calculi in this disease is technically challenging for urologists. The choice of treatment for urinary calculi in cases of crossed renal ectopia should be made depending on the size and position of the urinary calculi and the patient's anatomy.
Before proceeding to surgery, a preoperative assessment with contrast computed tomography is necessary to explore a solitary kidney with calculi so as not to miss the diagnosis of crossed fused renal ectopia because the management of renal stone in this rare malformation is complicated.
交叉融合肾异位是一种罕见的先天性异常,其特征是双肾在脊柱一侧融合在一起。在此,我们报告该疾病的一种非典型亚型。据我们所知,在当前文献中,右肾 superior crossed fused renal ectopia(此处 superior 可能有误,推测为高位交叉融合肾异位)的病例报道很少。
一名40岁1型糖尿病男性因糖尿病酮症酸中毒和腹痛就诊于我院,最初在内分泌科接受治疗,随后在CT扫描发现孤立右肾鹿角形结石后转至我院泌尿外科。在治疗过程中后来发现这是一例高位交叉融合肾异位。
单侧融合肾高位异位极为罕见,对于泌尿外科医生而言,治疗该疾病中的尿路结石在技术上具有挑战性。交叉肾异位病例中尿路结石的治疗选择应根据尿路结石的大小和位置以及患者的解剖结构来决定。
在进行手术之前,有必要进行对比增强计算机断层扫描的术前评估,以探查有结石的孤立肾,以免漏诊交叉融合肾异位,因为这种罕见畸形中肾结石的处理很复杂。