Suppr超能文献

猫叫综合征颅面短小综合征表型重叠谱。

Overlapping Spectrum of Craniofacial Microsomia Phenotype in Cat-Eye Syndrome.

机构信息

Laboratory of Human Cytogenetics and Cytogenomics, Department of Translational Medicine, School of Medical Sciences, State University of Campinas (Unicamp), Campinas, São Paulo, Brazil.

Faculty of Medicine, Federal University of Alagoas (UFAL), Maceió, Alagoas, Brazil.

出版信息

Cleft Palate Craniofac J. 2024 Sep;61(9):1578-1585. doi: 10.1177/10556656231174435. Epub 2023 May 14.

Abstract

This study reports three patients with Cat-eye Syndrome (CES), two of which present a previous clinical diagnosis of Craniofacial microsomia (CFM). Chromosomal microarray analysis (CMA) revealed a tetrasomy of 1,7 Mb at the 22q11.2q11.21 region, which is the typical region triplicated in the CES, in all patients. The most frequent craniofacial features found in individuals with CFM and CES are preauricular tags and/or pits and mandibular hypoplasia. We reinforce that the candidate genes for CFM features, particularly ear malformation, preauricular tags/pits, and facial asymmetry, can be in the proximal region of the 22q11.2 region.

摘要

本研究报道了三例猫眼综合征(CES)患者,其中两例之前临床诊断为颅面骨发育不全(CFM)。染色体微阵列分析(CMA)显示所有患者的 22q11.2q11.21 区域均存在 1,7Mb 的四体性,这是 CES 的典型重复区域。在患有 CFM 和 CES 的个体中,最常见的颅面特征是耳前赘生物和/或凹陷和下颌骨发育不全。我们强调,CFM 特征的候选基因,特别是耳部畸形、耳前赘生物/凹陷和面部不对称,可能位于 22q11.2 区域的近端。

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型,支持多种主流文档格式。

立即体验