Bhesania Natalie, Patil Deepa T, McCleary Brendan, Selvakumar Praveen Kumar Conjeevaram, Radhakrishnan Kadakkal
From the Division of Pediatric Gastroenterology, UMMC, Jackson, MS.
Department of Pathology, Brigham and Women's Hospital, Boston, MA.
JPGN Rep. 2023 Mar 9;4(2):e298. doi: 10.1097/PG9.0000000000000298. eCollection 2023 May.
We describe a case of segmental arterial mediolysis (SAM) in a 2-year-old male who presented with symptoms of acute pancreatitis. SAM is a vascular entity of unknown etiology that involves medium-sized arteries in which the integrity of the vessel wall is compromised, resulting in increased susceptibility to ischemia, hemorrhage, and dissection. The clinical presentation is variable and can range from abdominal pain to more ominous findings of abdominal hemorrhage or organ infarction. This entity should be considered in the correct clinical setting and after other vasculopathies have been excluded. We aim to bring awareness to pediatric providers given this is a rare entity with variable presentation, which could be potentially life threatening.
我们描述了一例2岁男性节段性动脉中层溶解（SAM）病例，该患儿表现为急性胰腺炎症状。SAM是一种病因不明的血管疾病，累及中动脉，血管壁完整性受损，导致缺血、出血和夹层形成的易感性增加。临床表现多样，可从腹痛到更严重的腹部出血或器官梗死表现。在正确的临床背景下且排除其他血管病变后应考虑这一疾病。鉴于这是一种表现多样的罕见疾病，可能会危及生命，我们旨在提高儿科医护人员的认识。
