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一例表现为回盲部肠套叠的巨大低度恶性阑尾黏液性肿瘤(LAMN):病例报告

A giant low-grade appendiceal mucinous neoplasm (LAMN) presenting as ileocecal intussusception: a case report.

作者信息

Liapis Stavros C, Perivoliotis Konstantinos, Psarianos Kyriakos, Chatzinikolaou Charito, Moula Amalia I, Skoufogiannis Pavlos, Balogiannis Ioannis, Lytras Dimitrios

机构信息

Department of Surgery, General Hospital of Volos, Magnesia, Greece.

Department of Pathology, General Hospital of Volos, Magnesia, Greece.

出版信息

J Surg Case Rep. 2023 May 27;2023(5):rjad273. doi: 10.1093/jscr/rjad273. eCollection 2023 May.

Abstract

We report the rare case of a giant low-grade appendiceal mucinous neoplasm (LAMN), presenting as ileocecal intussusception. An 80-year-old woman presented in the emergency department of our institution with progressively worsening diffuse abdominal pain during the last 24 h. A CT scan revealed a giant abdominal mass (98.7 × 127.3 × 107.6 mm) with air-fluid level and imaging characteristics of ileocecal intussusception. An emergency exploratory laparotomy was performed, and a well-circumscribed cystic mass deriving from the appendix was found. A right hemicolectomy was performed, and the histopathological examination confirmed the diagnosis of LAMN. This report aims to raise awareness among surgeons and radiologists, about LAMNs as a differential diagnosis of right iliac fossa masses presenting as acute abdomen.

摘要

我们报告了一例罕见的巨大低度阑尾黏液性肿瘤(LAMN),表现为回盲部肠套叠。一名80岁女性因在过去24小时内弥漫性腹痛逐渐加重,前来我院急诊科就诊。CT扫描显示一个巨大的腹部肿块(98.7×127.3×107.6mm),伴有气液平面,具有回盲部肠套叠的影像学特征。遂行急诊剖腹探查术,发现一个来自阑尾的边界清晰的囊性肿块。进行了右半结肠切除术,组织病理学检查确诊为LAMN。本报告旨在提高外科医生和放射科医生对LAMN的认识,将其作为表现为急腹症的右髂窝肿块的鉴别诊断。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d4e5/10224788/db56b556f507/rjad273f1.jpg

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