Oreto Lilia, Guccione Paolo, Gitto Placido, Bruno Letteria, Zanai Rosanna, Grasso Nadia, Iannace Enrico, Zito Concetta, Carerj Scipione, Agati Salvatore
Department of Clinical and Experimental Medicine, University of Messina, 98122 Messina, Italy.
Mediterranean Pediatric Cardiology Center, Bambino Gesù Children's Hospital, 98035 Taormina, Italy.
Children (Basel). 2023 Jun 4;10(6):1012. doi: 10.3390/children10061012.
Hypoplastic left heart syndrome is a spectrum of complex congenital cardiac defects. Although in borderline cases, biventricular repair is a viable option, in the majority of cases, univentricular palliation is the treatment of choice. Hybrid palliation can be a valid alternative to classic Norwood operation in the neonatal period, especially in selected cases such as high-risk patients or borderline left ventricles. Echocardiography is the main diagnostic modality in this pediatric population, from the fetal diagnosis to the subsequent surgical steps of palliative treatment. Hybrid palliation is performed after birth and is characterized by surgical banding of the pulmonary arteries along with transcatheter stenting of the ductus arteriosus. There are some peculiar aspects of cardiac imaging that characterize this type of palliation, and that should be considered in the different phases before and after the procedure. We aimed to review the current literature about the role of echocardiography in the management of patients with hypoplastic left heart undergoing hybrid palliation.
左心发育不全综合征是一系列复杂的先天性心脏缺陷。虽然在临界病例中,双心室修复是一种可行的选择,但在大多数情况下,单心室姑息治疗是首选的治疗方法。在新生儿期,杂交姑息治疗可以是经典诺伍德手术的有效替代方案,特别是在某些特定病例中,如高危患者或临界左心室。从胎儿诊断到后续姑息治疗的手术步骤,超声心动图是这一儿科人群的主要诊断方式。杂交姑息治疗在出生后进行,其特点是对肺动脉进行外科束带术并对动脉导管进行经导管支架置入术。心脏成像有一些特殊方面是这种姑息治疗的特征,并且在手术前后的不同阶段都应予以考虑。我们旨在综述当前关于超声心动图在接受杂交姑息治疗的左心发育不全患者管理中的作用的文献。