Department of Experimental Neurodegeneration, University Medical Center Göttingen, Göttingen, Germany.
J Neurochem. 2024 Aug;168(8):1426-1441. doi: 10.1111/jnc.15955. Epub 2023 Sep 11.
Protein quality control mechanisms oversee numerous aspects of protein lifetime. From the point of protein synthesis, protein homeostasis machineries take part in folding, solubilization, and/or degradation of impaired proteins. Some proteins follow an alternative path upon loss of their solubility, thus are secluded from the cytosol and form protein aggregates. Protein aggregates differ in their function and composition, rendering protein aggregation a complex phenomenon that continues to receive plenty of attention in the scientific and medical communities. Traditionally, protein aggregates have been associated with aging and a large spectrum of protein folding diseases, such as neurodegenerative diseases, type 2 diabetes, or cataract. However, a body of evidence suggests that they may act as an adaptive mechanism to overcome transient stressful conditions, serving as a sink for the removal of misfolded proteins from the cytosol or storage compartments for machineries required upon stress release. In this review, we present examples and evidence elaborating different possible roles of protein aggregation and discuss their potential roles in stress survival, aging, and disease, as well as possible anti-aggregation interventions.
蛋白质质量控制机制监督着蛋白质寿命的众多方面。从蛋白质合成的角度来看,蛋白质稳态机制参与了受损蛋白质的折叠、溶解和/或降解。一些蛋白质在失去可溶性后会选择另一种途径,从而被隔离在细胞质之外并形成蛋白质聚集体。蛋白质聚集体在功能和组成上存在差异,使得蛋白质聚集成为一个复杂的现象,在科学界和医学界继续受到广泛关注。传统上,蛋白质聚集体与衰老和广泛的蛋白质折叠疾病有关,如神经退行性疾病、2 型糖尿病或白内障。然而,越来越多的证据表明,它们可能作为一种适应性机制来克服短暂的应激条件,作为从细胞质中去除错误折叠蛋白质的汇或在应激释放时所需的机器的储存室。在这篇综述中,我们提出了不同的蛋白质聚集的可能作用的例子和证据,并讨论了它们在应激生存、衰老和疾病中的潜在作用,以及可能的抗聚集干预措施。