Malagic Polutak Maida, Hartel Mark
University Department of Medicine, Division of General Internal and Emergency Medicine, Cantonal Hospital Aarau, Aarau CH-5001, Switzerland.
Department of General and Visceral Surgery, Cantonal Hospital Aarau, Aarau CH-5001, Switzerland.
J Surg Case Rep. 2023 Nov 20;2023(11):rjad629. doi: 10.1093/jscr/rjad629. eCollection 2023 Nov.
Hemangioblastoma is a rare, benign, and morphologically distinctive tumor. In most cases, the tumor involves the central nervous system. Extraneural occurrences are rare, with just a few reports of hemangioblastoma situated outside of neural tissue, such as the retroperitoneum. We report a case of sporadic retroperitoneal hemangioblastoma in an 87-year-old male patient, diagnosed as an incidental finding in a CT scan performed because of kidney stone disease. The CT scan showed a mass in the retroperitoneum posterior to the inferior vena cava. The patient reported no remarkable symptoms. We describe our path to diagnosis, the possible differential diagnosis for retroperitoneal masses, and the histopathologic features of the tumor. There are <250 reported extra neuraxial hemangioblastomas and just 14 reported cases situated outside of the neural tissue. Our case is the eighth case report of a hemangioblastoma arising from the soft tissue of the retroperitoneum.
血管母细胞瘤是一种罕见的良性肿瘤,形态独特。多数情况下,该肿瘤累及中枢神经系统。神经外发生的情况罕见,仅有少数关于血管母细胞瘤位于神经组织外的报道,如腹膜后。我们报告一例87岁男性散发性腹膜后血管母细胞瘤病例,该病例是因肾结石疾病进行CT扫描时偶然发现的。CT扫描显示下腔静脉后方腹膜后有一肿块。患者无明显症状。我们描述了诊断过程、腹膜后肿块可能的鉴别诊断以及肿瘤的组织病理学特征。据报道,神经轴外血管母细胞瘤不足250例,位于神经组织外的仅有14例。我们的病例是腹膜后软组织来源血管母细胞瘤的第八例病例报告。