Department of Paediatric Cardiology, Children's Health Ireland at Crumlin, Crumlin, Dublin, Ireland.
Children's Health Ireland at Crumlin, Crumlin, Dublin, Ireland.
Cardiol Young. 2024 Jun;34(6):1232-1238. doi: 10.1017/S1047951123004249. Epub 2024 Jan 2.
CHD is a significant risk factor for the development of necrotising enterocolitis. Existing literature does not differentiate between term and preterm populations. Long-term outcomes of these patients are not well understood. The aim was to investigate the baseline characteristics and outcomes of term normal birth weight infants with CHD who developed necrotising enterocolitis.
A retrospective review was performed of infants from a single tertiary centre with CHD who developed necrotising enterocolitis of Bell's Stage 1-3, over a ten-year period. Inclusion criteria was those born greater than 36 weeks' gestation and birth weight over 2500g. Exclusion criteria included congenital gastro-intestinal abnormalities. Sub-group analysis was performed using Fisher's exact test.
Twenty-five patients were identified, with a median gestational age of 38 weeks. Patients with univentricular physiology accounted for 32% (n = 8) and 52% of patients (n = 13) had a duct-dependent lesion. Atrioventricular septal defect was the most common cardiac diagnosis (n = 6, 24%). Patients with trisomy 21 accounted for 20% of cases. Mortality within 30 days of necrotising enterocolitis was 20%. Long-term mortality was 40%, which increased with increasing Bell's Stage. In total, 36% (n = 9) required surgical management of necrotising enterocolitis, the rate of which was significantly higher in trisomy 21 cases (p < 0.05).
Not previously described in term infants is the high rate of trisomy 21 and atrioventricular septal defect. This may reflect higher baseline incidence in our population. Infants with trisomy 21 were more likely to develop surgical necrotising enterocolitis. Mortality at long-term follow-up was high in patients with Bell's Stage 2-3.
CHD 是坏死性小肠结肠炎发展的重要危险因素。现有文献并未区分足月和早产人群。这些患者的长期预后尚不清楚。本研究旨在探讨发生 Bell 1-3 期坏死性小肠结肠炎的足月正常出生体重 CHD 患儿的基线特征和结局。
对单中心十年间发生 Bell 1-3 期坏死性小肠结肠炎的足月(胎龄>36 周且出生体重>2500g)正常出生体重 CHD 患儿进行回顾性研究。纳入标准为胎龄>36 周且出生体重>2500g。排除标准为存在先天性胃肠道异常。采用 Fisher 确切检验进行亚组分析。
共纳入 25 例患儿,中位胎龄为 38 周。单心室患儿占 32%(n=8),依赖导管存活的患儿占 52%(n=13)。最常见的心脏诊断为房室间隔缺损(n=6,24%)。20%的患儿存在 21 三体。30 天内坏死性小肠结肠炎死亡率为 20%。长期死亡率为 40%,且随 Bell 分期增加而升高。总共有 36%(n=9)的患儿需要手术治疗坏死性小肠结肠炎,21 三体患儿的手术率显著更高(p<0.05)。
本研究首次报道了在足月患儿中,21 三体和房室间隔缺损的发病率较高。这可能反映了本研究人群中这些疾病的基础发病率较高。21 三体患儿更易发生手术性坏死性小肠结肠炎。Bell 2-3 期患儿的长期死亡率较高。