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[亚急性坏死性脑病, Leigh 病。附 1 例报告]

[Subacute necrotizing encephalopathy, Leigh's disease. Apropos of a case].

作者信息

Delisle M B, Netter J C, Peyrille F, Bouissou H

出版信息

Ann Pathol. 1985;5(4-5):313-7.

PMID:3833250
Abstract

Leigh's disease is a subacute metabolic encephalopathy characterized by bilateral and symmetrical lesions of basal ganglia, mid-brain and pons. Lesions are related to an abnormal pyruvate metabolism which mechanisms remain still uncertain. This disease is rare and the authors present a case with complete anatomic study.

摘要

Leigh病是一种亚急性代谢性脑病,其特征为基底节、中脑和脑桥的双侧对称性病变。病变与丙酮酸代谢异常有关,但其机制仍不明确。这种疾病很罕见,作者报告了一例进行了完整解剖学研究的病例。

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1
[Subacute necrotizing encephalopathy, Leigh's disease. Apropos of a case].[亚急性坏死性脑病, Leigh 病。附 1 例报告]
Ann Pathol. 1985;5(4-5):313-7.
2
[Leigh's subacute necrotizing encephalomyelopathy due to decreased activity of the pyruvate dehydrogenase complex].丙酮酸脱氢酶复合体活性降低所致 Leigh 亚急性坏死性脑脊髓病
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Infantile form of subacute necrotizing encephalomyelopathy (Leigh's disease).婴儿型亚急性坏死性脑脊髓病(利氏病)。
J Med Assoc Thai. 1987 Oct;70(10):596-603.
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Sural nerve biopsy studies in Leigh's subacute necrotizing encephalomyelopathy.腓肠神经活检研究在 Leigh 氏亚急性坏死性脑脊髓病中的应用
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[An adult case of Leigh's subacute necrotizing encephalomyelopathy].[一例成人 Leigh 亚急性坏死性脑脊髓病病例]
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[Diagnostic criteria in classical infantile subacute necrotizing encephalomyelopathy (Leigh's disease)].[经典型婴儿亚急性坏死性脑脊髓病( Leigh病)的诊断标准]
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[Leigh's syndrome].
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