与遗传性免疫缺陷相关的血管炎和血管病变：概述
Vasculitis and vasculopathy associated with inborn errors of immunity: an overview.
作者信息
Federici Silvia, Cinicola Bianca Laura, La Torre Francesco, Castagnoli Riccardo, Lougaris Vassilios, Giardino Giuliana, Volpi Stefano, Caorsi Roberta, Leonardi Lucia, Corrente Stefania, Soresina Annarosa, Cancrini Caterina, Insalaco Antonella, Gattorno Marco, De Benedetti Fabrizio, Marseglia Gian Luigi, Del Giudice Michele Miraglia, Cardinale Fabio
机构信息
Division of Rheumatology, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.
Department of Maternal Infantile and Urological Sciences, Sapienza University of Rome, Rome, Italy.
出版信息
Front Pediatr. 2024 Jan 31;11:1258301. doi: 10.3389/fped.2023.1258301. eCollection 2023.
Systemic autoinflammatory diseases (SAIDs) are disorders of innate immunity, which are characterized by unprovoked recurrent flares of systemic inflammation often characterized by fever associated with clinical manifestations mainly involving the musculoskeletal, mucocutaneous, gastrointestinal, and nervous systems. Several conditions also present with varied, sometimes prominent, involvement of the vascular system, with features of vasculitis characterized by variable target vessel involvement and organ damage. Here, we report a systematic review of vasculitis and vasculopathy associated with inborn errors of immunity.
系统性自身炎症性疾病（SAIDs）是先天性免疫紊乱疾病，其特征为无明显诱因的全身性炎症反复发作，常伴有发热，并伴有主要累及肌肉骨骼、皮肤黏膜、胃肠道和神经系统的临床表现。一些疾病还伴有血管系统的不同程度受累，有时受累较为显著，具有血管炎的特征，表现为不同的靶血管受累和器官损害。在此，我们报告一项关于与先天性免疫缺陷相关的血管炎和血管病变的系统综述。
Zotero 插件