Department of Biology and Biochemistry, South Kazakhstan Medical Academy, Shymkent, Kazakhstan.
Department of Clinical Rheumatology and Immunology, University Hospital in Krakow, Krakow, Poland.
Rheumatol Int. 2024 Jun;44(6):1003-1011. doi: 10.1007/s00296-024-05582-9. Epub 2024 Apr 8.
Systemic vasculitides are among the less common disorders encountered in routine rheumatology practice. The low incidence and heterogeneous presentation at onset can potentially lead to delayed diagnosis. Not recognizing these in the early phase may prove detrimental, as some vasculitis may progress to a catastrophic course with major morbidity or mortality. The causes of diagnostic delay may vary among different types of vasculitis and may also be disease-, patient-, or physician-related. Disease-related factors include the myriad presentations with diverse and non-specific symptoms, mimicking other conditions like infections. In addition, some forms have prolonged prodromal phases before evident organ damage. Limited awareness among healthcare professionals, particularly outside rheumatology, and a lack of readily available diagnostic tools contribute to missed diagnoses. Delays in seeking care due to non-specific symptoms or lack of access to specialist care can worsen outcomes. The economic burden also increases with delayed diagnosis and damage accrual when the disease remains unrecognized or untreated for prolonged periods. Although the causes of vasculitis are numerous, including secondary causes, in this review, we focus on diagnostic delays in primary vasculitides and suggest potential steps to identify and treat these diseases early. These include educating both healthcare professionals and the public about the signs and symptoms of vasculitis; expanding the rheumatology workforce and facilitating timely referrals; implementing readily available and reliable tests for early detection; and streamlining care and diagnostic pathways. Such measures have the potential to improve the overall outcomes of the disease, with prolonged remission, minimal damage accrual, and improved quality of life.
系统性血管炎是风湿科常见疾病之一。其发病率低,起病时表现多样,可能导致诊断延迟。如果在早期阶段未能识别出来,可能会产生不良后果,因为某些血管炎可能会进展为灾难性病程,导致严重的发病率或死亡率。诊断延迟的原因可能因不同类型的血管炎而异,也可能与疾病、患者或医生有关。与疾病相关的因素包括多种表现形式,具有不同且非特异性的症状,类似于感染等其他疾病。此外,某些类型在明显的器官损伤之前有较长的前驱期。医疗保健专业人员的认识有限,特别是在风湿科之外,以及缺乏现成的诊断工具,这导致了漏诊。由于非特异性症状或缺乏专科医疗资源,导致就诊延迟,会使预后恶化。诊断延迟和疾病持续未被识别或治疗,会导致损伤累积,从而增加了经济负担。虽然血管炎的病因很多,包括继发性病因,但在本次综述中,我们重点关注原发性血管炎的诊断延迟,并提出了一些潜在的方法,以早期识别和治疗这些疾病。这些方法包括教育医疗保健专业人员和公众了解血管炎的症状和体征;扩大风湿科的工作人员队伍并促进及时转诊;实施现成且可靠的检测方法以进行早期检测;以及简化护理和诊断流程。这些措施有可能改善疾病的整体预后,延长缓解期,减少损伤累积,并提高生活质量。